What kinds of defects can happen with CCHD?

What kinds of defects can happen with CCHD?

There are three different types of cyanotic heart disease:

Left heart obstructive lesions

These congenital heart defects reduce blood flow between your heart and the rest of your body (systemic blood flow). Specific conditions include:

• Hypoplastic left heart syndrome: Hypoplastic left heart syndrome (HLHS) involves underdeveloped structures in the left side of your heart. The left side of your heart is too small to pump enough blood to the rest of your body.
• Interrupted aortic arch: In interrupted aortic arch, your aorta is incomplete.

Right heart obstructive lesions

These congenital heart defects reduce blood flow between your heart and lungs (pulmonary flow). Specific conditions include:

• Pulmonary atresia: The pulmonary valve is like a door between the right side of your heart and lungs. With pulmonary atresia (PA), the pulmonary valve doesn’t develop correctly or is blocked.
• Tricuspid atresia: The tricuspid valve is between the two chambers (atrium and ventricle) on the right side of your heart. In tricuspid atresia, the valve is not formed correctly. A piece of solid tissue blocks blood flow from the right atrium to the right ventricle.
• Tetralogy of Fallot: Tetralogy of Fallot (TOF) is the most common CCHD. It involves four heart defects.

Mixing lesions

The third type of CCHD is called mixing lesions. These heart defects cause your body to mix pulmonary and systemic blood flow. Specific conditions include:

• Transposition of the great arteries: In this condition, the two main arteries that leave your heart (the main pulmonary artery and the aorta) are reversed. This defect is your second most common CCHD.
• Total anomalous pulmonary venous return (TAPVR): In a baby with TAPVR, oxygen-rich blood doesn’t go from their lungs to the left side of their heart, where it should. Instead, the blood goes to the right side of their heart.
• Truncus arteriosus: In truncus arteriosus, you have only one main artery to carry blood to your body and your lungs, instead of two separate arteries.